Arnold Strauss , MD

Medical Degree: Washington University St. Louis, MO, 1970

Residency: Children's Hospital - St. Louis St. Louis, MO,

Fellowship: Children's Hospital and Washington University - St. Louis St. Louis, MO,

Postdoctoral Fellowship: Merck, Sharp and Dohme Research Laboratories Rahway, NJ,

Pediatric Cardiology, Genetic Basis of Pediatric Heart Disease

Peer Reviewed Publications

STRAUSS,A.W.; STRAUSS,A.W.,Jr. (1952. ) Pseudomucinous cystadenocarcinoma of the ovary .American Journal of Obstetrics and Gynecology, , 64 (6 ) ,1382 -1384

Keating,J.P.; Lell,M.E.; Strauss,A.W.; Zarkowsky,H.; Smith,G.E. (1973. ) Infantile methemoglobinemia caused by carrot juice .The New England journal of medicine, , 288 (16 ) ,824 -826

Strauss,A.W.; Escobedo,M.; Goldring,D. (1974. ) Continuous monitoring of arterial oxygen tension in the newborn infant .The Journal of pediatrics, , 85 (2 ) ,254 -261

Strauss,A.W.; Goldring,D. (1974. ) Editorial: Valve replacement in acute rheumatic heart disease .The Journal of pediatrics, , 84 (5 ) ,786 -787

Strauss,A.W.; Goldring,D.; Kissane,J.; Hernandez,A.; Hartmann,A.F.; McKnight,C.R.; Weldon,C.S. (1974. ) Valve replacement in acute rheumatic heart disease .The Journal of thoracic and cardiovascular surgery, , 67 (4 ) ,659 -670

Strauss,A.W.; Santa-Maria,M.; Goldring,D. (1975. ) Constrictive pericarditis in children .American Journal of Diseases of Children (1960), , 129 (7 ) ,822 -826

Alderson,P.O.; Jost,R.G.; Strauss,A.W.; Boonvisut,S.; Markham,J. (1975. ) Radionuclide angiocardiography. Improved diagnosis and quantitation of left-to-right shunts using area ratio techniques in children .Circulation, , 51 (6 ) ,1136 -1143

Alberts,A.W.; Strauss,A.W.; Hennessy,S.; Vagelos,P.R. (1975. ) Regulation of synthesis of hepatic fatty acid synthetase: binding of fatty acid synthetase antibodies to polysomes .Proceedings of the National Academy of Sciences of the United States of America, , 72 (10 ) ,3956 -3960

Strauss,A.W.; Alberts,A.W.; Hennessy,S.; Vagelos,P.R. (1975. ) Regulation of synthesis of hepatic fatty acid synthetase: polysomal translation in a cell-free system .Proceedings of the National Academy of Sciences of the United States of America, , 72 (11 ) ,4366 -4370

Strauss,A.W.; Bennett,C.D.; Donohue,A.M.; Rodkey,J.A.; Alberts,A.W. (1977. ) Rat liver pre-proalbumin: complete amino acid sequence of the pre-piece. Analysis of the direct translation product of albumin messenger RNA .The Journal of biological chemistry, , 252 (19 ) ,6846 -6855

Strauss,A.W.; Donohue,A.M.; Bennett,C.D.; Rodkey,J.A.; Alberts,A.W. (1977. ) Rat liver preproalbumin: in vitro synthesis and partial amino acid sequence .Proceedings of the National Academy of Sciences of the United States of America, , 74 (4 ) ,1358 -1362

Strauss,A.W.; Bennett,C.A.; Donohue,A.M.; Rodkey,J.A.; Boime,I.; Alberts,A.W. (1978. ) Conversion of rat pre-proalbumin to proalbumin in vitro by ascites membranes. Demonstration by NH2-TERMINAL SEQUENCE ANALYSIS .The Journal of biological chemistry, , 253 (17 ) ,6270 -6274

Hernandez,A.; Strauss,A.W.; McKnight,R.; Hartmann,A.F.,Jr. (1978. ) Diagnosis of pulmonary arteriovenous fistula by contrast echocardiography .The Journal of pediatrics, , 93 (2 ) ,258 -261

Strauss,A.W.; Zimmerman,M.; Boime,I.; Ashe,B.; Mumford,R.A.; Alberts,A.W. (1979. ) Characterization of an endopeptidase involved in pre-protein processing .Proceedings of the National Academy of Sciences of the United States of America, , 76 (9 ) ,4225 -4229

Haymond,M.W.; Strauss,A.W.; Arnold,K.J.; Bier,D.M. (1979. ) Glucose homeostasis in children with severe cyanotic congenital heart disease .The Journal of pediatrics, , 95 (2 ) ,220 -227

Jones,L.A.; Jordan,D.K.; Taysi,K.; Strauss,A.W.; Toth,J.K. (1979. ) Partial duplication of the long arm of chromosome 5: a case due to balanced paternal translocation and review of the literature .Human genetics, , 51 (1 ) ,37 -42

Jones,L.A.; Taysi,K.; Strauss,A.W.; Hartmann,A.F. (1979. ) Partial trisomy 13 as a result of de novo (6p;13q) translocation .Human genetics, , 48 (2 ) ,245 -249

Taysi,K.; Noetzel,M.J.; Strauss,A.W. (1979. ) Presumptive long arm deletion of chromosome 8: a new syndrome? .Human genetics, , 51 (1 ) ,49 -53

Mumford,R.A.; Strauss,A.W.; Powers,J.C.; Pierzchala,P.A.; Nishino,N.; Zimmerman,M. (1980. ) A zinc metalloendopeptidase associated with dog pancreatic membranes .The Journal of biological chemistry, , 255 (6 ) ,2227 -2230

Strauss,A.W.; Zimmerman,M.; Mumford,R.A.; Alberts,A.W. (1980. ) Processing of pre-proalbumin and pre-placental lactogen .Annals of the New York Academy of Sciences, , 343 ,168 -179

Zimmerman,M.; Ashe,B.M.; Alberts,A.W.; Pierzchala,P.A.; Powers,J.C.; Nishino,N.; Strauss,A.W.; Mumford,R.A. (1980. ) Protease activities present in dog pancreatic membranes that process human pre-placental lactogen .Annals of the New York Academy of Sciences, , 343 ,405 -414

Henry,C.G.; Gutierrez,F.; Lee,J.T.; Hartmann,A.F.; Bell,M.J.; Bower,R.J.; Strauss,A.W. (1981. ) Aortic thrombosis presenting as congestive heart failure: an umbilical artery catheter complication .The Journal of pediatrics, , 98 (5 ) ,820 -822

Canter,C.E.; Bower,R.J.; Strauss,A.W. (1981. ) Atypical Kawasaki disease with aortic aneurysm .Pediatrics, , 68 (6 ) ,885 -888

Henry,C.G.; Strauss,A.W.; Keating,J.P.; Hillman,R.E. (1981. ) Congestive cardiomyopathy associated with beta-ketothiolase deficiency .The Journal of pediatrics, , 99 (5 ) ,754 -757

Graves,C.B.; Munns,T.W.; Carlisle,T.L.; Grant,G.A.; Strauss,A.W. (1981. ) Induction of prothrombin synthesis by prothrombin fragments .Proceedings of the National Academy of Sciences of the United States of America, , 78 (8 ) ,4772 -4776

Mumford,R.A.; Pickett,C.B.; Zimmerman,M.; Strauss,A.W. (1981. ) Protease activities present in wheat germ and rabbit reticulocyte lysates .Biochemical and biophysical research communications, , 103 (2 ) ,565 -572

Mumford,R.A.; Pierzchala,P.A.; Strauss,A.W.; Zimmerman,M. (1981. ) Purification of a membrane-bound metalloendopeptidase from porcine kidney that degrades peptide hormones .Proceedings of the National Academy of Sciences of the United States of America, , 78 (11 ) ,6623 -6627

Henry,C.G.; Goldring,D.; Hartmann,A.F.; Weldon,C.S.; Strauss,A.W. (1981. ) Treatment of d-transposition of the great arteries: management of hypoxemia after balloon atrial septostomy .The American Journal of Cardiology, , 47 (2 ) ,299 -306

Gordon,J.I.; Smith,D.P.; Alpers,D.H.; Strauss,A.W. (1982. ) Cloning of a complementary deoxyribonucleic acid encoding a portion of rat intestinal preapolipoprotein AIV messenger ribonucleic acid .Biochemistry, , 21 (22 ) ,5424 -5431

Strauss,A.W.; Boime,I. (1982. ) Compartmentation of newly synthesized proteins .CRC critical reviews in biochemistry, , 12 (3 ) ,205 -235

Gordon,J.I.; Smith,D.P.; Alpers,D.H.; Strauss,A.W. (1982. ) Proteolytic processing of the primary translation product of rat intestinal apolipoprotein A-IV mRNA. Comparison with preproapolipoprotein A-I processing .The Journal of biological chemistry, , 257 (14 ) ,8418 -8423

Graves,C.B.; Munns,T.W.; Willingham,A.K.; Strauss,A.W. (1982. ) Rat factor X is synthesized as a single chain precursor inducible by prothrombin fragments .The Journal of biological chemistry, , 257 (21 ) ,13108 -13113

Taysi,K.; Strauss,A.W.; Yang,V.; Padmalatha,C.; Marshall,R.E. (1982. ) Terminal deletion of the long arm of chromosome 10 : q26 to qter. Case report and review of literature .Annales de Genetique, , 25 (3 ) ,141 -144

Gordon,J.I.; Smith,D.P.; Andy,R.; Alpers,D.H.; Schonfeld,G.; Strauss,A.W. (1982. ) The primary translation product of rat intestinal apolipoprotein A-I mRNA is an unusual preproprotein .The Journal of biological chemistry, , 257 (2 ) ,971 -978

Gordon,J.I.; Budelier,K.A.; Sims,H.F.; Edelstein,C.; Scanu,A.M.; Strauss,A.W. (1983. ) Biosynthesis of human preproapolipoprotein A-II .The Journal of biological chemistry, , 258 (22 ) ,14054 -14059

Edelstein,C.; Gordon,J.I.; Toscas,K.; Sims,H.F.; Strauss,A.W.; Scanu,A.M. (1983. ) In vitro conversion of proapoprotein A-I to apoprotein A-I. Partial characterization of an extracellular enzyme activity .The Journal of biological chemistry, , 258 (19 ) ,11430 -11433

Perryman,M.B.; Strauss,A.W.; Olson,J.; Roberts,R. (1983. ) In vitro translation of canine mitochondrial creatine kinase messenger RNA .Biochemical and biophysical research communications, , 110 (3 ) ,967 -972

Perryman,M.B.; Strauss,A.W.; Buettner,T.L.; Roberts,R. (1983. ) Molecular heterogeneity of creatine kinase isoenzymes .Biochimica et biophysica acta, , 747 (3 ) ,284 -290

Gordon,J.I.; Sims,H.F.; Lentz,S.R.; Edelstein,C.; Scanu,A.M.; Strauss,A.W. (1983. ) Proteolytic processing of human preproapolipoprotein A-I. A proposed defect in the conversion of pro A-I to A-I in Tangier's disease .The Journal of biological chemistry, , 258 (6 ) ,4037 -4044

Cockerham,J.T.; Martin,T.C.; Gutierrez,F.R.; Hartmann,A.F.,Jr; Goldring,D.; Strauss,A.W. (1983. ) Spontaneous closure of secundum atrial septal defect in infants and young children .The American Journal of Cardiology, , 52 (10 ) ,1267 -1271

Gordon,J.I.; Alpers,D.H.; Ockner,R.K.; Strauss,A.W. (1983. ) The nucleotide sequence of rat liver fatty acid binding protein mRNA .The Journal of biological chemistry, , 258 (5 ) ,3356 -3363

Leonard,W.J.; Strauss,A.W.; Go,M.F.; Alpers,D.H.; Gordon,J.I. (1984. ) Biosynthesis and compartmentalization of rat-intestinal vitamin-D-dependent calcium-binding protein .European journal of biochemistry / FEBS, , 139 (3 ) ,561 -571

Blaufuss,M.C.; Gordon,J.I.; Schonfeld,G.; Strauss,A.W.; Alpers,D.H. (1984. ) Biosynthesis of apolipoprotein C-III in rat liver and small intestinal mucosa .The Journal of biological chemistry, , 259 (4 ) ,2452 -2456

Gordon,J.I.; Bisgaier,C.L.; Sims,H.F.; Sachdev,O.P.; Glickman,R.M.; Strauss,A.W. (1984. ) Biosynthesis of human preapolipoprotein A-IV .The Journal of biological chemistry, , 259 (1 ) ,468 -474

Alpers,D.H.; Strauss,A.W.; Ockner,R.K.; Bass,N.M.; Gordon,J.I. (1984. ) Cloning of a cDNA encoding rat intestinal fatty acid binding protein .Proceedings of the National Academy of Sciences of the United States of America, , 81 (2 ) ,313 -317

Lowe,J.B.; Strauss,A.W.; Gordon,J.I. (1984. ) Expression of a mammalian fatty acid-binding protein in Escherichia coli .The Journal of biological chemistry, , 259 (20 ) ,12696 -12704

Gordon,J.I.; Sims,H.F.; Edelstein,C.; Scanu,A.M.; Strauss,A.W. (1984. ) Human proapolipoprotein A-II is cleaved following secretion from Hep G2 cells by a thiol protease .The Journal of biological chemistry, , 259 (24 ) ,15556 -15563

Hashimoto,H.; Grace,A.M.; Billadello,J.J.; Gross,R.W.; Strauss,A.W.; Sobel,B.E. (1984. ) Nondenaturing quantification of subforms of canine MM creatine kinase isoenzymes (isoforms) and their interconversion .The Journal of laboratory and clinical medicine, , 103 (3 ) ,470 -484

Hashimoto,H.; Abendschein,D.R.; Strauss,A.W.; Sobel,B.E. (1985. ) Early detection of myocardial infarction in conscious dogs by analysis of plasma MM creatine kinase isoforms .Circulation, , 71 (2 ) ,363 -369

Gordon,J.I.; Sims,H.F.; Edelstein,C.; Scanu,A.M.; Strauss,A.W. (1985. ) Extracellular processing of proapolipoprotein A-II in Hep G2 cell cultures is mediated by a 54-kDa protease immunologically related to cathepsin B .The Journal of biological chemistry, , 260 (27 ) ,14824 -14831

Grace,A.M.; Strauss,A.W.; Sobel,B.E. (1985. ) Sensitive quantification of isoforms of canine MM creatine kinase with an immunoblot procedure suitable for large numbers of samples .Analytical Biochemistry, , 149 (1 ) ,209 -217

Billadello,J.J.; Roman,D.G.; Grace,A.M.; Sobel,B.E.; Strauss,A.W. (1985. ) The nature of post-translational formation of MM creatine kinase isoforms .The Journal of biological chemistry, , 260 (28 ) ,14988 -14992

Hortin,G.; Folz,R.; Gordon,J.I.; Strauss,A.W. (1986. ) Characterization of sites of tyrosine sulfation in proteins and criteria for predicting their occurrence .Biochemical and biophysical research communications, , 141 (1 ) ,326 -333

Hortin,G.; Strauss,A.W. (1986. ) Effects of acidotropic compounds on the secretory pathway: inhibition of secretion and processing of the third and fourth components of complement .Biochemical and biophysical research communications, , 136 (2 ) ,603 -609

Ovitt,C.E.; Strauss,A.W.; Alpers,D.H.; Chou,J.Y.; Boime,I. (1986. ) Expression of different-sized placental alkaline phosphatase mRNAs in placenta and choriocarcinoma cells .Proceedings of the National Academy of Sciences of the United States of America, , 83 (11 ) ,3781 -3785

Hortin,G.; Sims,H.; Strauss,A.W. (1986. ) Identification of the site of sulfation of the fourth component of human complement .The Journal of biological chemistry, , 261 (4 ) ,1786 -1793

Hortin,G.; Tollefsen,D.M.; Strauss,A.W. (1986. ) Identification of two sites of sulfation of human heparin cofactor II .The Journal of biological chemistry, , 261 (34 ) ,15827 -15830

Alpers,D.H.; Helms,D.; Seetharam,S.; May,V.L.; Strauss,A.W. (1986. ) In vitro translation of intestinal sucrase-isomaltase and glucoamylase .Biochemical and biophysical research communications, , 134 (1 ) ,37 -43

Grant,P.M.; Tellam,J.; May,V.L.; Strauss,A.W. (1986. ) Isolation and nucleotide sequence of a cDNA clone encoding rat mitochondrial malate dehydrogenase .Nucleic acids research, , 14 (15 ) ,6053 -6066

Gordon,J.I.; Sims,H.F.; Strauss,A.W.; Scanu,A.M.; Edelstein,C.; Byrne,R.E. (1986. ) Proteolytic processing and compartmentalization of the primary translation products of mammalian apolipoprotein mRNAs .CRC critical reviews in biochemistry, , 20 (1 ) ,37 -71

Canter,C.E.; Martin,T.C.; Spray,T.L.; Weldon,C.S.; Strauss,A.W. (1986. ) Scimitar syndrome in childhood .The American Journal of Cardiology, , 58 (7 ) ,652 -654

Hortin,G.; Chan,A.C.; Fok,K.F.; Strauss,A.W.; Atkinson,J.P. (1986. ) Sequence analysis of the COOH terminus of the alpha-chain of the fourth component of human complement. Identification of the site of its extracellular cleavage .The Journal of biological chemistry, , 261 (19 ) ,9065 -9069

Hortin,G.; Green,E.D.; Baenziger,J.U.; Strauss,A.W. (1986. ) Sulphation of proteins secreted by a human hepatoma-derived cell line. Sulphation of N-linked oligosaccharides on alpha 2HS-glycoprotein .The Biochemical journal, , 235 (2 ) ,407 -414

Billadello,J.J.; Kelly,D.P.; Roman,D.G.; Strauss,A.W. (1986. ) The complete nucleotide sequence of canine brain B creatine kinase mRNA: homology in the coding and 3' noncoding regions among species .Biochemical and biophysical research communications, , 138 (1 ) ,392 -398

Grant,P.M.; Roderick,S.L.; Grant,G.A.; Banaszak,L.J.; Strauss,A.W. (1987. ) Comparison of the precursor and mature forms of rat heart mitochondrial malate dehydrogenase .Biochemistry, , 26 (1 ) ,128 -134

Abendschein,D.R.; Serota,H.; Plummer,T.H.,Jr; Amiraian,K.; Strauss,A.W.; Sobel,B.E.; Jaffe,A.S. (1987. ) Conversion of MM creatine kinase isoforms in human plasma by carboxypeptidase N .The Journal of laboratory and clinical medicine, , 110 (6 ) ,798 -806

Seetharam,S.; Ovitt,C.; Strauss,A.W.; Rubin,D.; Alpers,D.H. (1987. ) Fat feeding stimulates only one of the two mRNAs encoding rat intestinal membranous and secreted alkaline phosphatase .Biochemical and biophysical research communications, , 145 (1 ) ,363 -368

Chu,T.W.; Grant,P.M.; Strauss,A.W. (1987. ) Mutation of a neutral amino acid in the transit peptide of rat mitochondrial malate dehydrogenase abolishes binding and import .The Journal of biological chemistry, , 262 (32 ) ,15759 -15764

Kelly,D.P.; Kim,J.J.; Billadello,J.J.; Hainline,B.E.; Chu,T.W.; Strauss,A.W. (1987. ) Nucleotide sequence of medium-chain acyl-CoA dehydrogenase mRNA and its expression in enzyme-deficient human tissue .Proceedings of the National Academy of Sciences of the United States of America, , 84 (12 ) ,4068 -4072

Grace,A.M.; Gualdoni,J.; Strauss,A.W.; Sobel,B.E. (1987. ) Quantification of isoforms of plasma MM creatine kinase (CK) with an immunoblot procedure .Catheterization and cardiovascular diagnosis, , 13 (1 ) ,26 -32

Hortin,G.; Fok,K.F.; Toren,P.C.; Strauss,A.W. (1987. ) Sulfation of a tyrosine residue in the plasmin-binding domain of alpha 2-antiplasmin .The Journal of biological chemistry, , 262 (7 ) ,3082 -3085

Chu,T.W.; Grant,P.M.; Strauss,A.W. (1987. ) The role of arginine residues in the rat mitochondrial malate dehydrogenase transit peptide .The Journal of biological chemistry, , 262 (26 ) ,12806 -12811

Trask,R.V.; Strauss,A.W.; Billadello,J.J. (1988. ) Developmental regulation and tissue-specific expression of the human muscle creatine kinase gene .The Journal of biological chemistry, , 263 (32 ) ,17142 -17149

Griffin,M.L.; Hernandez,A.; Martin,T.C.; Goldring,D.; Bolman,R.M.; Spray,T.L.; Strauss,A.W. (1988. ) Dilated cardiomyopathy in infants and children .Journal of the American College of Cardiology, , 11 (1 ) ,139 -144

Stallings,R.L.; Olson,E.; Strauss,A.W.; Thompson,L.H.; Bachinski,L.L.; Siciliano,M.J. (1988. ) Human creatine kinase genes on chromosomes 15 and 19, and proximity of the gene for the muscle form to the genes for apolipoprotein C2 and excision repair .American Journal of Human Genetics, , 43 (2 ) ,144 -151

Sztul,E.S.; Chu,T.W.; Strauss,A.W.; Rosenberg,L.E. (1988. ) Import of the malate dehydrogenase precursor by mitochondria. Cleavage within leader peptide by matrix protease leads to formation of intermediate-sized form .The Journal of biological chemistry, , 263 (24 ) ,12085 -12091

Billadello,J.J.; Fontanet,H.L.; Strauss,A.W.; Abendschein,D.R. (1989. ) Characterization of MB creatine kinase isoform conversion in vitro and in vivo in dogs .The Journal of clinical investigation, , 83 (5 ) ,1637 -1643

Lowe,M.E.; Rosenblum,J.L.; Strauss,A.W. (1989. ) Cloning and characterization of human pancreatic lipase cDNA .The Journal of biological chemistry, , 264 (33 ) ,20042 -20048

Haas,R.C.; Korenfeld,C.; Zhang,Z.F.; Perryman,B.; Roman,D.; Strauss,A.W. (1989. ) Isolation and characterization of the gene and cDNA encoding human mitochondrial creatine kinase .The Journal of biological chemistry, , 264 (5 ) ,2890 -2897

Gast,M.J.; Sims,H.F.; Murdock,G.L.; Gast,P.M.; Strauss,A.W. (1989. ) Isolation and sequencing of a complementary deoxyribonucleic acid clone encoding human placental 17 beta-estradiol dehydrogenase: identification of the putative cofactor binding site .American Journal of Obstetrics and Gynecology, , 161 (6 Pt 1 ) ,1726 -1731

Chu,T.W.; Eftime,R.; Sztul,E.; Strauss,A.W. (1989. ) Synthetic transit peptides inhibit import and processing of mitochondrial precursor proteins .The Journal of biological chemistry, , 264 (16 ) ,9552 -9558

Kelly,D.P.; Gordon,J.I.; Alpers,R.; Strauss,A.W. (1989. ) The tissue-specific expression and developmental regulation of two nuclear genes encoding rat mitochondrial proteins. Medium chain acyl-CoA dehydrogenase and mitochondrial malate dehydrogenase .The Journal of biological chemistry, , 264 (32 ) ,18921 -18925

Sztul,E.S.; Chu,T.W.; Strauss,A.W.; Rosenberg,L.E. (1989. ) Translocation of precursor proteins into the mitochondrial matrix occurs through an environment accessible to aqueous perturbants .Journal of cell science, , 94 ( Pt 4) (Pt 4 ) ,695 -701

Bross,P.; Engst,S.; Strauss,A.W.; Kelly,D.P.; Rasched,I.; Ghisla,S. (1990. ) Characterization of wild-type and an active site mutant of human medium chain acyl-CoA dehydrogenase after expression in Escherichia coli .The Journal of biological chemistry, , 265 (13 ) ,7116 -7119

Agrawal,H.C.; Agrawal,D.; Strauss,A.W. (1990. ) Cleavage of the P0 glycoprotein of the rat peripheral nerve myelin: tentative identification of cleavage site and evidence for the precursor-product relationship .Neurochemical research, , 15 (10 ) ,993 -1001

Lowe,M.E.; Rosenblum,J.L.; McEwen,P.; Strauss,A.W. (1990. ) Cloning and characterization of the human colipase cDNA .Biochemistry, , 29 (3 ) ,823 -828

Strauss,A.W.; Goldring,D. (1990. ) Coarctation of the aorta in infants .Circulation, , 82 (5 ) ,1882

Lowe,M.E.; Strauss,A.W. (1990. ) Expression of a Nagao-type, phosphatidylinositol-glycan anchored alkaline phosphatase in human choriocarcinomas .Cancer research, , 50 (13 ) ,3956 -3962

Long,C.A.; Bauer,G.S.; Lowe,M.E.; Strauss,A.W.; Gast,M.J. (1990. ) Isolation and characterization of the gene from a human genome encoding 17 beta-estradiol dehydrogenase: a comparison of Jar and BeWo choriocarcinoma cell lines .American Journal of Obstetrics and Gynecology, , 163 (6 Pt 1 ) ,1976 -1981

Strauss,A.W.; Duran,M.; Zhang,Z.F.; Alpers,R.; Kelly,D.P. (1990. ) Molecular analysis of medium chain acyl-CoA dehydrogenase deficiency .Progress in clinical and biological research, , 321 ,609 -623

Kelly,D.P.; Whelan,A.J.; Ogden,M.L.; Alpers,R.; Zhang,Z.F.; Bellus,G.; Gregersen,N.; Dorland,L.; Strauss,A.W. (1990. ) Molecular characterization of inherited medium-chain acyl-CoA dehydrogenase deficiency .Proceedings of the National Academy of Sciences of the United States of America, , 87 (23 ) ,9236 -9240

Lowe,M.; Strauss,A.W.; Alpers,R.; Seetharam,S.; Alpers,D.H. (1990. ) Molecular cloning and expression of a cDNA encoding the membrane-associated rat intestinal alkaline phosphatase .Biochimica et biophysica acta, , 1037 (2 ) ,170 -177

Haas,R.C.; Strauss,A.W. (1990. ) Separate nuclear genes encode sarcomere-specific and ubiquitous human mitochondrial creatine kinase isoenzymes .The Journal of biological chemistry, , 265 (12 ) ,6921 -6927

Kelly,D.P.; Strauss,A.W. (1990. ) The tissue-specific and developmental regulation of expression of rat medium-chain acyl-CoA dehydrogenase mRNA .Progress in clinical and biological research, , 321 ,599 -608

Gregersen,N.; Andresen,B.S.; Bross,P.; Winter,V.; Rudiger,N.; Engst,S.; Ghisla,S.; Christensen,E.; Kelly,D.; Strauss,A.W. (1991. ) Characterization of a disease-causing Lys329 to Glu mutation in 16 patients with medium-chain acyl-CoA dehydrogenase deficiency .Journal of inherited metabolic disease, , 14 (3 ) ,314 -316

Shackelford,P.G.; Strauss,A.W. (1991. ) Kawasaki syndrome .The New England journal of medicine, , 324 (23 ) ,1664 -1666

Gregersen,N.; Andresen,B.S.; Bross,P.; Winter,V.; Rudiger,N.; Engst,S.; Christensen,E.; Kelly,D.; Strauss,A.W.; Kolvraa,S. (1991. ) Molecular characterization of medium-chain acyl-CoA dehydrogenase (MCAD) deficiency: identification of a lys329 to glu mutation in the MCAD gene, and expression of inactive mutant enzyme protein in E. coli .Human genetics, , 86 (6 ) ,545 -551

Murphy,A.M.; Jones,L.,2nd; Sims,H.F.; Strauss,A.W. (1991. ) Molecular cloning of rat cardiac troponin I and analysis of troponin I isoform expression in developing rat heart .Biochemistry, , 30 (3 ) ,707 -712

Fontanet,H.L.; Trask,R.V.; Haas,R.C.; Strauss,A.W.; Abendschein,D.R.; Billadello,J.J. (1991. ) Regulation of expression of M, B, and mitochondrial creatine kinase mRNAs in the left ventricle after pressure overload in rats .Circulation research, , 68 (4 ) ,1007 -1012

Klein,S.C.; Haas,R.C.; Perryman,M.B.; Billadello,J.J.; Strauss,A.W. (1991. ) Regulatory element analysis and structural characterization of the human sarcomeric mitochondrial creatine kinase gene .The Journal of biological chemistry, , 266 (27 ) ,18058 -18065

Payne,R.M.; Haas,R.C.; Strauss,A.W. (1991. ) Structural characterization and tissue-specific expression of the mRNAs encoding isoenzymes from two rat mitochondrial creatine kinase genes .Biochimica et biophysica acta, , 1089 (3 ) ,352 -361

Ghisla,S.; Engst,S.; Moll,M.; Bross,P.; Strauss,A.W.; Kim,J.J. (1992. ) Alpha, beta-dehydrogenation by acyl-CoA dehydrogenases: role of functional groups at the active center .Progress in clinical and biological research, , 375 ,127 -142

Raisher,B.D.; Grant,J.W.; Martin,T.C.; Strauss,A.W.; Spray,T.L. (1992. ) Complete repair of total anomalous pulmonary venous connection in infancy .The Journal of thoracic and cardiovascular surgery, , 104 (2 ) ,443 -448

Kelly,D.P.; Zhang,Z.; Raisher,B.D.; Ogden,M.L.; Strauss,A.W. (1992. ) Identification and characterization of the 5' regulatory region of the human medium-chain acyl-CoA dehydrogenase (MCAD) gene .Progress in clinical and biological research, , 375 ,143 -149

Raisher,B.D.; Gulick,T.; Zhang,Z.; Strauss,A.W.; Moore,D.D.; Kelly,D.P. (1992. ) Identification of a novel retinoid-responsive element in the promoter region of the medium chain acyl-coenzyme A dehydrogenase gene .The Journal of biological chemistry, , 267 (28 ) ,20264 -20269

Kelly,D.P.; Hale,D.E.; Rutledge,S.L.; Ogden,M.L.; Whelan,A.J.; Zhang,Z.; Strauss,A.W. (1992. ) Molecular basis of inherited medium-chain acyl-CoA dehydrogenase deficiency causing sudden child death .Journal of inherited metabolic disease, , 15 (2 ) ,171 -180

Kelly,D.P.; Whelan,A.J.; Hale,D.E.; Rinaldo,P.; Rutledge,S.L.; Zhang,Z.; Strauss,A.W. (1992. ) Molecular characterization of medium-chain acyl-CoA dehydrogenase deficiency causing sudden death .Progress in clinical and biological research, , 375 ,463 -472

Tanaka,K.; Yokota,I.; Coates,P.M.; Strauss,A.W.; Kelly,D.P.; Zhang,Z.; Gregersen,N.; Andresen,B.S.; Matsubara,Y.; Curtis,D. (1992. ) Mutations in the medium chain acyl-CoA dehydrogenase (MCAD) gene .Human mutation, , 1 (4 ) ,271 -279

Su,C.Y.; Payne,M.; Strauss,A.W.; Dillmann,W.H. (1992. ) Selective reduction of creatine kinase subunit mRNAs in striated muscle of diabetic rats .The American Journal of Physiology, , 263 (2 Pt 1 ) ,E310 -6

Zhang,Z.F.; Kelly,D.P.; Kim,J.J.; Zhou,Y.Q.; Ogden,M.L.; Whelan,A.J.; Strauss,A.W. (1992. ) Structural organization and regulatory regions of the human medium-chain acyl-CoA dehydrogenase gene .Biochemistry, , 31 (1 ) ,81 -89

Andresen,B.S.; Kolvraa,S.; Bross,P.; Bolund,L.; Curtis,D.; Eiberg,H.; Zhang,Z.; Kelly,D.P.; Strauss,A.W.; Gregersen,N. (1993. ) A silent A to G mutation in exon 11 of the medium-chain acyl-CoA dehydrogenase (MCAD) gene .Human molecular genetics, , 2 (4 ) ,488

Payne,R.M.; Friedman,D.L.; Grant,J.W.; Perryman,M.B.; Strauss,A.W. (1993. ) Creatine kinase isoenzymes are highly regulated during pregnancy in rat uterus and placenta .The American Journal of Physiology, , 265 (4 Pt 1 ) ,E624 -35

Whelan,A.J.; Strauss,A.W.; Hale,D.E.; Mendelsohn,N.J.; Kelly,D.P. (1993. ) Expression and characterization of human mutant (glutamic acid304) medium-chain acyl-coenzyme A dehydrogenase in mammalian cells .Pediatric research, , 34 (5 ) ,694 -697

Johnson,M.C.; Canter,C.E.; Strauss,A.W.; Spray,T.L. (1993. ) Repair of coarctation of the aorta in infancy: comparison of surgical and balloon angioplasty .American Heart Journal, , 125 (2 Pt 1 ) ,464 -468

Zhang,Z.; Kolvraa,S.; Zhou,Y.; Kelly,D.P.; Gregersen,N.; Strauss,A.W. (1993. ) Three RFLPs defining a haplotype associated with the common mutation in human medium-chain acyl-CoA dehydrogenase (MCAD) deficiency occur in Alu repeats .American Journal of Human Genetics, , 52 (6 ) ,1111 -1121

Hainline,B.E.; Kahlenbeck,D.J.; Grant,J.; Strauss,A.W. (1993. ) Tissue specific and developmental expression of rat long-and medium-chain acyl-CoA dehydrogenases .Biochimica et biophysica acta, , 1216 (3 ) ,460 -468

Brackett,J.C.; Sims,H.F.; Steiner,R.D.; Nunge,M.; Zimmerman,E.M.; deMartinville,B.; Rinaldo,P.; Slaugh,R.; Strauss,A.W. (1994. ) A novel mutation in medium chain acyl-CoA dehydrogenase causes sudden neonatal death .The Journal of clinical investigation, , 94 (4 ) ,1477 -1483

Payne,R.M.; Strauss,A.W. (1994. ) Developmental expression of sarcomeric and ubiquitous mitochondrial creatine kinase is tissue-specific .Biochimica et biophysica acta, , 1219 (1 ) ,33 -38

O'Shea,D.L.; Gast,M.J.; Murdock,G.L.; Payne,R.M.; Strauss,A.W. (1994. ) Expression of engineered human 17 beta-estradiol dehydrogenase in a prokaryotic system .Journal of the Society for Gynecologic Investigation, , 1 (2 ) ,143 -149

Payne,R.M.; Strauss,A.W. (1994. ) Expression of the mitochondrial creatine kinase genes .Molecular and cellular biochemistry, , 133-134 ,235 -243

Djordjevic,S.; Dong,Y.; Paschke,R.; Frerman,F.E.; Strauss,A.W.; Kim,J.J. (1994. ) Identification of the catalytic base in long chain acyl-CoA dehydrogenase .Biochemistry, , 33 (14 ) ,4258 -4264

Kelly,D.P.; Strauss,A.W. (1994. ) Inherited cardiomyopathies .The New England journal of medicine, , 330 (13 ) ,913 -919

Johnson,M.C.; Strauss,A.W. (1994. ) The jury is still out regarding balloon therapy for native aortic coarctation .Journal of the American College of Cardiology, , 24 (6 ) ,1589 -1590

Johnson,M.C.; Watson,M.S.; Strauss,A.W.; Spray,T.L. (1995. ) Anomalous origin of the right pulmonary artery from the aorta and CATCH 22 syndrome .The Annals of Thoracic Surgery, , 60 (3 ) ,681 -2; discussion 682-3

Johnson,M.C.; Strauss,A.W.; Dowton,S.B.; Spray,T.L.; Huddleston,C.B.; Wood,M.K.; Slaugh,R.A.; Watson,M.S. (1995. ) Deletion within chromosome 22 is common in patients with absent pulmonary valve syndrome .The American Journal of Cardiology, , 76 (1 ) ,66 -69

Weinberger,M.J.; Rinaldo,P.; Strauss,A.W.; Bennett,M.J. (1995. ) Intact alpha-subunit is required for membrane-binding of human mitochondrial trifunctional beta-oxidation protein, but is not necessary for conferring 3-ketoacyl-CoA thiolase activity to the beta-subunit .Biochemical and biophysical research communications, , 209 (1 ) ,47 -52

Ziadeh,R.; Hoffman,E.P.; Finegold,D.N.; Hoop,R.C.; Brackett,J.C.; Strauss,A.W.; Naylor,E.W. (1995. ) Medium chain acyl-CoA dehydrogenase deficiency in Pennsylvania: neonatal screening shows high incidence and unexpected mutation frequencies .Pediatric research, , 37 (5 ) ,675 -678

Strauss,A.W.; Powell,C.K.; Hale,D.E.; Anderson,M.M.; Ahuja,A.; Brackett,J.C.; Sims,H.F. (1995. ) Molecular basis of human mitochondrial very-long-chain acyl-CoA dehydrogenase deficiency causing cardiomyopathy and sudden death in childhood .Proceedings of the National Academy of Sciences of the United States of America, , 92 (23 ) ,10496 -10500

Peterson,K.L.; Sergienko,E.E.; Wu,Y.; Kumar,N.R.; Strauss,A.W.; Oleson,A.E.; Muhonen,W.W.; Shabb,J.B.; Srivastava,D.K. (1995. ) Recombinant human liver medium-chain acyl-CoA dehydrogenase: purification, characterization, and the mechanism of interactions with functionally diverse C8-CoA molecules .Biochemistry, , 34 (45 ) ,14942 -14953

Johnson,M.C.; Payne,R.M.; Grant,J.W.; Strauss,A.W. (1995. ) The genetic basis of paediatric heart disease .Annals of Medicine, , 27 (3 ) ,289 -300

Leone,T.C.; Cresci,S.; Carter,M.E.; Zhang,Z.; Lala,D.S.; Strauss,A.W.; Kelly,D.P. (1995. ) The human medium chain Acyl-CoA dehydrogenase gene promoter consists of a complex arrangement of nuclear receptor response elements and Sp1 binding sites .The Journal of biological chemistry, , 270 (27 ) ,16308 -16314

Leone,T.C.; Cresci,S.; Carter,M.E.; Zhang,Z.; Lala,D.S.; Strauss,A.W.; Kelly,D.P. (1995. ) The human medium chain acyl-CoA dehydrogenase gene promoter consists of a complex arrangement of nuclear receptor response elements and Sp1 binding sites .The Journal of biological chemistry, , 270 (41 ) ,24622

Sims,H.F.; Brackett,J.C.; Powell,C.K.; Treem,W.R.; Hale,D.E.; Bennett,M.J.; Gibson,B.; Shapiro,S.; Strauss,A.W. (1995. ) The molecular basis of pediatric long chain 3-hydroxyacyl-CoA dehydrogenase deficiency associated with maternal acute fatty liver of pregnancy .Proceedings of the National Academy of Sciences of the United States of America, , 92 (3 ) ,841 -845

Payne,R.M.; Johnson,M.C.; Grant,J.W.; Strauss,A.W. (1995. ) Toward a molecular understanding of congenital heart disease .Circulation, , 91 (2 ) ,494 -504

Brackett,J.C.; Sims,H.F.; Rinaldo,P.; Shapiro,S.; Powell,C.K.; Bennett,M.J.; Strauss,A.W. (1995. ) Two alpha subunit donor splice site mutations cause human trifunctional protein deficiency .The Journal of clinical investigation, , 95 (5 ) ,2076 -2082

Johnson,M.C.; Watson,M.S.; Strauss,A.W. (1996. ) Chromosome 22q11 monosomy and the genetic basis of congenital heart disease .The Journal of pediatrics, , 129 (1 ) ,1 -3

Isaacs,J.D.,Jr; Sims,H.F.; Powell,C.K.; Bennett,M.J.; Hale,D.E.; Treem,W.R.; Strauss,A.W. (1996. ) Maternal acute fatty liver of pregnancy associated with fetal trifunctional protein deficiency: molecular characterization of a novel maternal mutant allele .Pediatric research, , 40 (3 ) ,393 -398

Bromberg,B.I.; Mazziotti,M.V.; Canter,C.E.; Spray,T.L.; Strauss,A.W.; Foglia,R.P. (1996. ) Recognition and management of nonpenetrating cardiac trauma in children .The Journal of pediatrics, , 128 (4 ) ,536 -541

Strauss,A.W.; Johnson,M.C. (1996. ) The genetic basis of pediatric cardiovascular disease .Seminars in perinatology, , 20 (6 ) ,564 -576

Eder,M.; Krautle,F.; Dong,Y.; Vock,P.; Kieweg,V.; Kim,J.J.; Strauss,A.W.; Ghisla,S. (1997. ) Characterization of human and pig kidney long-chain-acyl-CoA dehydrogenases and their role in beta-oxidation .European journal of biochemistry / FEBS, , 245 (3 ) ,600 -607

Qin,W.; Khuchua,Z.; Klein,S.C.; Strauss,A.W. (1997. ) Elements regulating cardiomyocyte expression of the human sarcomeric mitochondrial creatine kinase gene in transgenic mice .The Journal of biological chemistry, , 272 (40 ) ,25210 -25216

Zhang,Z.; Zhou,Y.; Mendelsohn,N.J.; Bauer,G.S.; Strauss,A.W. (1997. ) Regulation of the human long chain acyl-CoA dehydrogenase gene by nuclear hormone receptor transcription factors .Biochimica et biophysica acta, , 1350 (1 ) ,53 -64

Ibdah,J.A.; Tein,I.; Dionisi-Vici,C.; Bennett,M.J.; IJlst,L.; Gibson,B.; Wanders,R.J.; Strauss,A.W. (1998. ) Mild trifunctional protein deficiency is associated with progressive neuropathy and myopathy and suggests a novel genotype-phenotype correlation .The Journal of clinical investigation, , 102 (6 ) ,1193 -1199

Qin,W.; Khuchua,Z.; Cheng,J.; Boero,J.; Payne,R.M.; Strauss,A.W. (1998. ) Molecular characterization of the creatine kinases and some historical perspectives .Molecular and cellular biochemistry, , 184 (1-2 ) ,153 -167

Khuchua,Z.A.; Qin,W.; Boero,J.; Cheng,J.; Payne,R.M.; Saks,V.A.; Strauss,A.W. (1998. ) Octamer formation and coupling of cardiac sarcomeric mitochondrial creatine kinase are mediated by charged N-terminal residues .The Journal of biological chemistry, , 273 (36 ) ,22990 -22996

Benson,D.W.; Sharkey,A.; Fatkin,D.; Lang,P.; Basson,C.T.; McDonough,B.; Strauss,A.W.; Seidman,J.G.; Seidman,C.E. (1998. ) Reduced penetrance, variable expressivity, and genetic heterogeneity of familial atrial septal defects .Circulation, , 97 (20 ) ,2043 -2048

Strauss,A.W. (1998. ) The molecular basis of congenital cardiac disease .1 ,179 -188

Ibdah,J.A.; Bennett,M.J.; Rinaldo,P.; Zhao,Y.; Gibson,B.; Sims,H.F.; Strauss,A.W. (1999. ) A fetal fatty-acid oxidation disorder as a cause of liver disease in pregnant women .The New England journal of medicine, , 340 (22 ) ,1723 -1731

Barycki,J.J.; O'Brien,L.K.; Bratt,J.M.; Zhang,R.; Sanishvili,R.; Strauss,A.W.; Banaszak,L.J. (1999. ) Biochemical characterization and crystal structure determination of human heart short chain L-3-hydroxyacyl-CoA dehydrogenase provide insights into catalytic mechanism .Biochemistry, , 38 (18 ) ,5786 -5798

Zhou,Y.; Kelly,D.P.; Strauss,A.W.; Sims,H.; Zhang,Z. (1999. ) Characterization of the human very-long-chain acyl-CoA dehydrogenase gene promoter region: a role for activator protein 2 .Molecular genetics and metabolism, , 68 (4 ) ,481 -487

Matern,D.; Strauss,A.W.; Hillman,S.L.; Mayatepek,E.; Millington,D.S.; Trefz,F.K. (1999. ) Diagnosis of mitochondrial trifunctional protein deficiency in a blood spot from the newborn screening card by tandem mass spectrometry and DNA analysis .Pediatric research, , 46 (1 ) ,45 -49

Strauss,A.W.; Bennett,M.J.; Rinaldo,P.; Sims,H.F.; O'Brien,L.K.; Zhao,Y.; Gibson,B.; Ibdah,J. (1999. ) Inherited long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency and a fetal-maternal interaction cause maternal liver disease and other pregnancy complications .Seminars in perinatology, , 23 (2 ) ,100 -112

Ibdah,J.A.; Dasouki,M.J.; Strauss,A.W. (1999. ) Long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency: variable expressivity of maternal illness during pregnancy and unusual presentation with infantile cholestasis and hypocalcaemia .Journal of inherited metabolic disease, , 22 (7 ) ,811 -814

Mathur,A.; Sims,H.F.; Gopalakrishnan,D.; Gibson,B.; Rinaldo,P.; Vockley,J.; Hug,G.; Strauss,A.W. (1999. ) Molecular heterogeneity in very-long-chain acyl-CoA dehydrogenase deficiency causing pediatric cardiomyopathy and sudden death .Circulation, , 99 (10 ) ,1337 -1343

Qin,W.; Khuchua,Z.; Boero,J.; Payne,R.M.; Strauss,A.W. (1999. ) Oxidative myocytes of heart and skeletal muscle express abundant sarcomeric mitochondrial creatine kinase .The Histochemical journal, , 31 (6 ) ,357 -365

Barycki,J.J.; O'Brien,L.K.; Birktoft,J.J.; Strauss,A.W.; Banaszak,L.J. (1999. ) Pig heart short chain L-3-hydroxyacyl-CoA dehydrogenase revisited: sequence analysis and crystal structure determination .Protein science : a publication of the Protein Society, , 8 (10 ) ,2010 -2018

Hahn,S.H.; Lee,E.H.; Jung,J.W.; Hong,C.H.; Yoon,H.R.; Rinaldo,P.; Sims,H.; Gibson,B.; Strauss,A.W. (1999. ) Very long chain acyl coenzyme A dehydrogenase deficiency in a 5-month-old Korean boy: identification of a novel mutation .The Journal of pediatrics, , 135 (2 Pt 1 ) ,250 -253

Schlattner,U.; Eder,M.; Dolder,M.; Khuchua,Z.A.; Strauss,A.W.; Wallimann,T. (2000. ) Divergent enzyme kinetics and structural properties of the two human mitochondrial creatine kinase isoenzymes .Biological chemistry, , 381 (11 ) ,1063 -1070

Bennett,M.J.; Rinaldo,P.; Strauss,A.W. (2000. ) Inborn errors of mitochondrial fatty acid oxidation .Critical reviews in clinical laboratory sciences, , 37 (1 ) ,1 -44

Barycki,J.J.; O'Brien,L.K.; Strauss,A.W.; Banaszak,L.J. (2000. ) Sequestration of the active site by interdomain shifting. Crystallographic and spectroscopic evidence for distinct conformations of L-3-hydroxyacyl-CoA dehydrogenase .The Journal of biological chemistry, , 275 (35 ) ,27186 -27196

Jones,P.M.; Moffitt,M.; Joseph,D.; Harthcock,P.A.; Boriack,R.L.; Ibdah,J.A.; Strauss,A.W.; Bennett,M.J. (2001. ) Accumulation of free 3-hydroxy fatty acids in the culture media of fibroblasts from patients deficient in long-chain l-3-hydroxyacyl-CoA dehydrogenase: a useful diagnostic aid .Clinical chemistry, , 47 (7 ) ,1190 -1194

Albers,S.; Levy,H.L.; Irons,M.; Strauss,A.W.; Marsden,D. (2001. ) Compound heterozygosity in four asymptomatic siblings with medium-chain acyl-CoA dehydrogenase deficiency .Journal of inherited metabolic disease, , 24 (3 ) ,417 -418

Wood,J.C.; Magera,M.J.; Rinaldo,P.; Seashore,M.R.; Strauss,A.W.; Friedman,A. (2001. ) Diagnosis of very long chain acyl-dehydrogenase deficiency from an infant's newborn screening card .Pediatrics, , 108 (1 ) ,E19

Barycki,J.J.; O'Brien,L.K.; Strauss,A.W.; Banaszak,L.J. (2001. ) Glutamate 170 of human l-3-hydroxyacyl-CoA dehydrogenase is required for proper orientation of the catalytic histidine and structural integrity of the enzyme .The Journal of biological chemistry, , 276 (39 ) ,36718 -36726

Ibdah,J.A.; Paul,H.; Zhao,Y.; Binford,S.; Salleng,K.; Cline,M.; Matern,D.; Bennett,M.J.; Rinaldo,P.; Strauss,A.W. (2001. ) Lack of mitochondrial trifunctional protein in mice causes neonatal hypoglycemia and sudden death .The Journal of clinical investigation, , 107 (11 ) ,1403 -1409

Ibdah,J.A.; Zhao,Y.; Viola,J.; Gibson,B.; Bennett,M.J.; Strauss,A.W. (2001. ) Molecular prenatal diagnosis in families with fetal mitochondrial trifunctional protein mutations .The Journal of pediatrics, , 138 (3 ) ,396 -399

Matern,D.; Schehata,B.M.; Shekhawa,P.; Strauss,A.W.; Bennett,M.J.; Rinaldo,P. (2001. ) Placental floor infarction complicating the pregnancy of a fetus with long-chain 3-hydroxyacyl-CoA dehydrogenase (LCHAD) deficiency .Molecular genetics and metabolism, , 72 (3 ) ,265 -268

Woodside,K.J.; Knisely,A.S.; Strauss,A.W.; Gugliuzza,K.K.; Daller,J.A. (2001. ) Progression of hepatic damage during cold storage after procurement in a liver and kidney donor with HELLP syndrome .Transplantation, , 72 (12 ) ,1990 -1993

Yoon,H.R.; Strauss,A.W.; Yoo,H.W. (2001. ) Sudden death in a Korean infant with very long-chain acyl-CoA dehydrogenase deficiency .Journal of inherited metabolic disease, , 24 (3 ) ,407 -408

Zytkovicz,T.H.; Fitzgerald,E.F.; Marsden,D.; Larson,C.A.; Shih,V.E.; Johnson,D.M.; Strauss,A.W.; Comeau,A.M.; Eaton,R.B.; Grady,G.F. (2001. ) Tandem mass spectrometric analysis for amino, organic, and fatty acid disorders in newborn dried blood spots: a two-year summary from the New England Newborn Screening Program .Clinical chemistry, , 47 (11 ) ,1945 -1955

Straussberg,R.; Strauss,A.W. (2002. ) A novel mutation of late-onset very-long-chain acyl-CoA dehydrogenase deficiency .Pediatric neurology, , 27 (2 ) ,136 -137

Yang,Z.; Zhao,Y.; Bennett,M.J.; Strauss,A.W.; Ibdah,J.A. (2002. ) Fetal genotypes and pregnancy outcomes in 35 families with mitochondrial trifunctional protein mutations .American Journal of Obstetrics and Gynecology, , 187 (3 ) ,715 -720

Yang,Z.; Yamada,J.; Zhao,Y.; Strauss,A.W.; Ibdah,J.A. (2002. ) Prospective screening for pediatric mitochondrial trifunctional protein defects in pregnancies complicated by liver disease .JAMA : the journal of the American Medical Association, , 288 (17 ) ,2163 -2166

Spiekerkoetter,U.; Eeds,A.; Yue,Z.; Haines,J.; Strauss,A.W.; Summar,M. (2002. ) Uniparental disomy of chromosome 2 resulting in lethal trifunctional protein deficiency due to homozygous alpha-subunit mutations .Human mutation, , 20 (6 ) ,447 -451

Lee,J.E.; Yoon,H.R.; Paik,K.H.; Hwang,S.J.; Shim,J.W.; Chang,Y.S.; Park,W.S.; Strauss,A.W.; Jin,D.K. (2003. ) A case of mitochondrial trifunctional protein deficiency diagnosed by acylcarnitine profile and DNA analysis in a dried blood spot of a 4-day-old boy .Journal of inherited metabolic disease, , 26 (4 ) ,403 -406

Khuchua,Z.; Wozniak,D.F.; Bardgett,M.E.; Yue,Z.; McDonald,M.; Boero,J.; Hartman,R.E.; Sims,H.; Strauss,A.W. (2003. ) Deletion of the N-terminus of murine map2 by gene targeting disrupts hippocampal ca1 neuron architecture and alters contextual memory .Neuroscience, , 119 (1 ) ,101 -111

Shekhawat,P.; Bennett,M.J.; Sadovsky,Y.; Nelson,D.M.; Rakheja,D.; Strauss,A.W. (2003. ) Human placenta metabolizes fatty acids: implications for fetal fatty acid oxidation disorders and maternal liver diseases .American journal of physiology.Endocrinology and metabolism, , 284 (6 ) ,E1098 -105

Spiekerkoetter,U.; Sun,B.; Khuchua,Z.; Bennett,M.J.; Strauss,A.W. (2003. ) Molecular and phenotypic heterogeneity in mitochondrial trifunctional protein deficiency due to beta-subunit mutations .Human mutation, , 21 (6 ) ,598 -607

Spiekerkoetter,U.; Sun,B.; Zytkovicz,T.; Wanders,R.; Strauss,A.W.; Wendel,U. (2003. ) MS/MS-based newborn and family screening detects asymptomatic patients with very-long-chain acyl-CoA dehydrogenase deficiency .The Journal of pediatrics, , 143 (3 ) ,335 -342

Boero,J.; Qin,W.; Cheng,J.; Woolsey,T.A.; Strauss,A.W.; Khuchua,Z. (2003. ) Restricted neuronal expression of ubiquitous mitochondrial creatine kinase: changing patterns in development and with increased activity .Molecular and cellular biochemistry, , 244 (1-2 ) ,69 -76

Exil,V.J.; Roberts,R.L.; Sims,H.; McLaughlin,J.E.; Malkin,R.A.; Gardner,C.D.; Ni,G.; Rottman,J.N.; Strauss,A.W. (2003. ) Very-long-chain acyl-coenzyme a dehydrogenase deficiency in mice .Circulation research, , 93 (5 ) ,448 -455

Spiekerkoetter,U.; Tokunaga,C.; Wendel,U.; Mayatepek,E.; Exil,V.; Duran,M.; Wijburg,F.A.; Wanders,R.J.; Strauss,A.W. (2004. ) Changes in blood carnitine and acylcarnitine profiles of very long-chain acyl-CoA dehydrogenase-deficient mice subjected to stress .European journal of clinical investigation, , 34 (3 ) ,191 -196

Spiekerkoetter,U.; Khuchua,Z.; Yue,Z.; Bennett,M.J.; Strauss,A.W. (2004. ) General mitochondrial trifunctional protein (TFP) deficiency as a result of either alpha- or beta-subunit mutations exhibits similar phenotypes because mutations in either subunit alter TFP complex expression and subunit turnover .Pediatric research, , 55 (2 ) ,190 -196

Tsirka,A.E.; Trinkaus,K.; Chen,S.C.; Lipshultz,S.E.; Towbin,J.A.; Colan,S.D.; Exil,V.; Strauss,A.W.; Canter,C.E. (2004. ) Improved outcomes of pediatric dilated cardiomyopathy with utilization of heart transplantation .Journal of the American College of Cardiology, , 44 (2 ) ,391 -397

Tyni,T.; Paetau,A.; Strauss,A.W.; Middleton,B.; Kivela,T. (2004. ) Mitochondrial fatty acid beta-oxidation in the human eye and brain: implications for the retinopathy of long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency .Pediatric research, , 56 (5 ) ,744 -750

Spiekerkoetter,U.; Bennett,M.J.; Ben-Zeev,B.; Strauss,A.W.; Tein,I. (2004. ) Peripheral neuropathy, episodic myoglobinuria, and respiratory failure in deficiency of the mitochondrial trifunctional protein .Muscle & nerve, , 29 (1 ) ,66 -72

McKinney,J.T.; Longo,N.; Hahn,S.H.; Matern,D.; Rinaldo,P.; Strauss,A.W.; Dobrowolski,S.F. (2004. ) Rapid, comprehensive screening of the human medium chain acyl-CoA dehydrogenase gene .Molecular genetics and metabolism, , 82 (2 ) ,112 -120

Strauss,A.W. (2004. ) Tandem mass spectrometry in discovery of disorders of the metabolome .The Journal of clinical investigation, , 113 (3 ) ,354 -356

Spierkerkoetter,U.; Khuchua,Z.; Yue,Z.; Strauss,A.W. (2004. ) The early-onset phenotype of mitochondrial trifunctional protein deficiency: a lethal disorder with multiple tissue involvement .Journal of inherited metabolic disease, , 27 (2 ) ,294 -296

Djouadi,F.; Aubey,F.; Schlemmer,D.; Ruiter,J.P.; Wanders,R.J.; Strauss,A.W.; Bastin,J. (2005. ) Bezafibrate increases very-long-chain acyl-CoA dehydrogenase protein and mRNA expression in deficient fibroblasts and is a potential therapy for fatty acid oxidation disorders .Human molecular genetics, , 14 (18 ) ,2695 -2703

Shekhawat,P.S.; Matern,D.; Strauss,A.W. (2005. ) Fetal fatty acid oxidation disorders, their effect on maternal health and neonatal outcome: impact of expanded newborn screening on their diagnosis and management .Pediatric research, , 57 (5 Pt 2 ) ,78R -86R

Strauss,A.W. (2005. ) Surprising? Perhaps not. Long-chain fatty acid oxidation during human fetal development .Pediatric research, , 57 (6 ) ,753 -754

Spiekerkoetter,U.; Tokunaga,C.; Wendel,U.; Mayatepek,E.; Ijlst,L.; Vaz,F.M.; van Vlies,N.; Overmars,H.; Duran,M.; Wijburg,F.A.; Wanders,R.J.; Strauss,A.W. (2005. ) Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice .Pediatric research, , 57 (6 ) ,760 -764

Khuchua,Z.; Yue,Z.; Batts,L.; Strauss,A.W. (2006. ) A zebrafish model of human Barth syndrome reveals the essential role of tafazzin in cardiac development and function .Circulation research, , 99 (2 ) ,201 -208

Exil,V.J.; Gardner,C.D.; Rottman,J.N.; Sims,H.; Bartelds,B.; Khuchua,Z.; Sindhal,R.; Ni,G.; Strauss,A.W. (2006. ) Abnormal mitochondrial bioenergetics and heart rate dysfunction in mice lacking very-long-chain acyl-CoA dehydrogenase .American journal of physiology.Heart and circulatory physiology, , 290 (3 ) ,H1289 -97

Liebig,M.; Gyenes,M.; Brauers,G.; Ruiter,J.P.; Wendel,U.; Mayatepek,E.; Strauss,A.W.; Wanders,R.J.; Spiekerkoetter,U. (2006. ) Carnitine supplementation induces long-chain acylcarnitine production--studies in the VLCAD-deficient mouse .Journal of inherited metabolic disease, , 29 (2-3 ) ,343 -344

Spiekerkoetter,U.; Ruiter,J.; Tokunaga,C.; Wendel,U.; Mayatepek,E.; Wijburg,F.A.; Strauss,A.W.; Wanders,R.J. (2006. ) Evidence for impaired gluconeogenesis in very long-chain acyl-CoA dehydrogenase-deficient mice .Hormone and metabolic research.Hormon- und Stoffwechselforschung.Hormones et metabolisme, , 38 (10 ) ,625 -630

Liebig,M.; Schymik,I.; Mueller,M.; Wendel,U.; Mayatepek,E.; Ruiter,J.; Strauss,A.W.; Wanders,R.J.; Spiekerkoetter,U. (2006. ) Neonatal screening for very long-chain acyl-coA dehydrogenase deficiency: enzymatic and molecular evaluation of neonates with elevated C14:1-carnitine levels .Pediatrics, , 118 (3 ) ,1065 -1069

Schymik,I.; Liebig,M.; Mueller,M.; Wendel,U.; Mayatepek,E.; Strauss,A.W.; Wanders,R.J.; Spiekerkoetter,U. (2006. ) Pitfalls of neonatal screening for very-long-chain acyl-CoA dehydrogenase deficiency using tandem mass spectrometry .The Journal of pediatrics, , 149 (1 ) ,128 -130

Djouadi,F.; Aubey,F.; Schlemmer,D.; Gobin,S.; Laforet,P.; Wanders,R.J.; Strauss,A.W.; Bonnefont,J.P.; Bastin,J. (2006. ) Potential of fibrates in the treatment of fatty acid oxidation disorders: revival of classical drugs? .Journal of inherited metabolic disease, , 29 (2-3 ) ,341 -342

Liske,M.R.; Greeley,C.S.; Law,D.J.; Reich,J.D.; Morrow,W.R.; Baldwin,H.S.; Graham,T.P.; Strauss,A.W.; Kavanaugh-McHugh,A.L.; Walsh,W.F.; Tennessee Task Force on Screening Newborn Infants for Critical Congenital Heart Disease. (2006. ) Report of the Tennessee Task Force on Screening Newborn Infants for Critical Congenital Heart Disease .Pediatrics, , 118 (4 ) ,e1250 -6

Bennett,M.J.; Russell,L.K.; Tokunaga,C.; Narayan,S.B.; Tan,L.; Seegmiller,A.; Boriack,R.L.; Strauss,A.W. (2006. ) Reye-like syndrome resulting from novel missense mutations in mitochondrial medium- and short-chain l-3-hydroxy-acyl-CoA dehydrogenase .Molecular genetics and metabolism, , 89 (1-2 ) ,74 -79

Hoffman,J.D.; Steiner,R.D.; Paradise,L.; Harding,C.O.; Ding,L.; Strauss,A.W.; Kaplan,P. (2006. ) Rhabdomyolysis in the military: recognizing late-onset very long-chain acyl Co-A dehydrogenase deficiency .Military medicine, , 171 (7 ) ,657 -658

Werdich,A.A.; Baudenbacher,F.; Dzhura,I.; Jeyakumar,L.H.; Kannankeril,P.J.; Fleischer,S.; Legrone,A.; Milatovic,D.; Aschner,M.; Strauss,A.W.; Anderson,M.; Exil,V.J. (2007. ) Polymorphic Ventricular Tachycardia and Abnormal Calcium Handling in Very-Long-Chain Acyl-CoA Dehydrogenase Null Mice .American Journal of Physiology. Heart and Circulatory Physiology, ,

Acehan, Devrim; Vaz, Frederic; Houtkooper, Riekelt H; James, Jeanne; Moore, Vicky; Tokunaga, Chonan; Kulik, Willem; Wansapura, Janaka; Toth, Matthew J; Strauss, Arnold; Khuchua, Zaza (2011. ) Cardiac and skeletal muscle defects in a mouse model of human Barth syndrome.The Journal of biological chemistry, , 286 (2 ) ,899-908 More Information

Li, Changhong; Chen, Pan; Palladino, Andrew; Narayan, Srinivas; Russell, Laurie K; Sayed, Samir; Xiong, Guoxiang; Chen, Jie; Stokes, David; Butt, Yasmeen M; Jones, Patricia M; Collins, Heather W; Cohen, Noam A; Cohen, Akiva S; Nissim, Itzhak; Smith, Thomas J; Strauss, Arnold W; Matschinsky, Franz M; Bennett, Michael J; Stanley, Charles A (2010. ) Mechanism of hyperinsulinism in short-chain 3-hydroxyacyl-CoA dehydrogenase deficiency involves activation of glutamate dehydrogenase.The Journal of biological chemistry, , 285 (41 ) ,31806-18 More Information

Britigan, Bradley; Strauss, Arnold; Susman, Jeff (2010. ) Salami science or editorial imperialism?.The Journal of pediatrics, , 157 (3 ) ,518-9; author reply More Information

Arnold, Georgianne L; Van Hove, Johan; Freedenberg, Debra; Strauss, Arnold; Longo, Nicola; Burton, Barbara; Garganta, Cheryl; Ficicioglu, Can; Cederbaum, Stephen; Harding, Cary; Boles, Richard G; Matern, Dietrich; Chakraborty, Pranesh; Feigenbaum, Annette (2009. ) A Delphi clinical practice protocol for the management of very long chain acyl-CoA dehydrogenase deficiency.Molecular genetics and metabolism, , 96 (3 ) ,85-90 More Information

Hsu, Ho-Wen; Zytkovicz, Thomas H; Comeau, Anne Marie; Strauss, Arnold W; Marsden, Deborah; Shih, Vivian E; Grady, George F; Eaton, Roger B (2008. ) Spectrum of medium-chain acyl-CoA dehydrogenase deficiency detected by newborn screening.Pediatrics, , 121 (5 ) ,e1108-14 More Information

Chappell, Tresa; Creech, C Buddy; Parra, David; Strauss, Arnold; Scholl, Frank; Whitney, Gina (2008. ) Presentation of pulmonary artery intimal sarcoma in an infant with a history of neonatal valvular pulmonic stenosis.The Annals of thoracic surgery, , 85 (3 ) ,1092-4 More Information

Werdich, Andreas A; Baudenbacher, Franz; Dzhura, Igor; Jeyakumar, Loice H; Kannankeril, Prince J; Fleischer, Sidney; LeGrone, Alison; Milatovic, Dejan; Aschner, Michael; Strauss, Arnold W; Anderson, Mark E; Exil, Vernat J (2007. ) Polymorphic ventricular tachycardia and abnormal Ca2+ handling in very-long-chain acyl-CoA dehydrogenase null mice.American journal of physiology. Heart and circulatory physiology, , 292 (5 ) ,H2202-11 More Information

Liske, Michael R; Greeley, Christopher S; Law, David J; Reich, Jonathan D; Morrow, William R; Baldwin, H Scott; Graham, Thomas P; Strauss, Arnold W; Kavanaugh-McHugh, Ann L; Walsh, William F (2006. ) Report of the Tennessee Task Force on Screening Newborn Infants for Critical Congenital Heart Disease.Pediatrics, , 118 (4 ) ,e1250-6 More Information

Bennett, Michael J; Russell, Laurie K; Tokunaga, Chonan; Narayan, Srinivas B; Tan, Lu; Seegmiller, Adam; Boriack, Richard L; Strauss, Arnold W Reye-like syndrome resulting from novel missense mutations in mitochondrial medium- and short-chain l-3-hydroxy-acyl-CoA dehydrogenase.Molecular genetics and metabolism, , 89 (1-2 ) ,74-9 More Information

Liebig, Michaela; Schymik, Ina; Mueller, Martina; Wendel, Udo; Mayatepek, Ertan; Ruiter, Jos; Strauss, Arnold W; Wanders, Ronald J A; Spiekerkoetter, Ute (2006. ) Neonatal screening for very long-chain acyl-coA dehydrogenase deficiency: enzymatic and molecular evaluation of neonates with elevated C14:1-carnitine levels.Pediatrics, , 118 (3 ) ,1065-9 More Information

Khuchua, Zaza; Yue, Zou; Batts, Lorene; Strauss, Arnold W (2006. ) A zebrafish model of human Barth syndrome reveals the essential role of tafazzin in cardiac development and function.Circulation research, , 99 (2 ) ,201-8 More Information

Schymik, Ina; Liebig, Michaela; Mueller, Martina; Wendel, Udo; Mayatepek, Ertan; Strauss, Arnold W; Wanders, Ronald J A; Spiekerkoetter, Ute (2006. ) Pitfalls of neonatal screening for very-long-chain acyl-CoA dehydrogenase deficiency using tandem mass spectrometry.The Journal of pediatrics, , 149 (1 ) ,128-30 More Information

Hoffman, Jodi D; Steiner, Robert D; Paradise, Lori; Harding, Carey O; Ding, Li; Strauss, Arnold W; Kaplan, Paige (2006. ) Rhabdomyolysis in the military: recognizing late-onset very long-chain acyl Co-A dehydrogenase deficiency. Military medicine, , 171 (7 ) ,657-8

Exil, Vernat J; Gardner, Carla D; Rottman, Jeffrey N; Sims, Harold; Bartelds, Beatrijs; Khuchua, Zaza; Sindhal, Rekha; Ni, Gemin; Strauss, Arnold W (2006. ) Abnormal mitochondrial bioenergetics and heart rate dysfunction in mice lacking very-long-chain acyl-CoA dehydrogenase.American journal of physiology. Heart and circulatory physiology, , 290 (3 ) ,H1289-97 More Information

Strauss, Arnold W (2005. ) Surprising? Perhaps not. Long-chain fatty acid oxidation during human fetal development.Pediatric research, , 57 (6 ) ,753-4 More Information

Spiekerkoetter, Ute; Tokunaga, Chonan; Wendel, Udo; Mayatepek, Ertan; Ijlst, Lodewijk; Vaz, Frederic M; van Vlies, Naomi; Overmars, Henk; Duran, Marinus; Wijburg, Frits A; Wanders, Ronald J; Strauss, Arnold W (2005. ) Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice.Pediatric research, , 57 (6 ) ,760-4 More Information

Shekhawat, Prem S; Matern, Dietrich; Strauss, Arnold W (2005. ) Fetal fatty acid oxidation disorders, their effect on maternal health and neonatal outcome: impact of expanded newborn screening on their diagnosis and management.Pediatric research, , 57 (5 Pt 2 ) ,78R-86R More Information

Tyni, Tiina; Paetau, Anders; Strauss, Arnold W; Middleton, Bruce; Kivelä, Tero (2004. ) Mitochondrial fatty acid beta-oxidation in the human eye and brain: implications for the retinopathy of long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency.Pediatric research, , 56 (5 ) ,744-50 More Information

Tsirka, Anna E; Trinkaus, Kathryn; Chen, Su-Chiung; Lipshultz, Steven E; Towbin, Jeffrey A; Colan, Steven D; Exil, Vernat; Strauss, Arnold W; Canter, Charles E (2004. ) Improved outcomes of pediatric dilated cardiomyopathy with utilization of heart transplantation.Journal of the American College of Cardiology, , 44 (2 ) ,391-7 More Information

Strauss, Arnold W (2004. ) Tandem mass spectrometry in discovery of disorders of the metabolome.The Journal of clinical investigation, , 113 (3 ) ,354-6 More Information

Spiekerkoetter, Ute; Khuchua, Zaza; Yue, Zou; Bennett, Michael J; Strauss, Arnold W (2004. ) General mitochondrial trifunctional protein (TFP) deficiency as a result of either alpha- or beta-subunit mutations exhibits similar phenotypes because mutations in either subunit alter TFP complex expression and subunit turnover.Pediatric research, , 55 (2 ) ,190-6 More Information

Spiekerkoetter, Ute; Bennett, Michael J; Ben-Zeev, Bruria; Strauss, Arnold W; Tein, Ingrid (2004. ) Peripheral neuropathy, episodic myoglobinuria, and respiratory failure in deficiency of the mitochondrial trifunctional protein.Muscle & nerve, , 29 (1 ) ,66-72 More Information

Exil, Vernat J; Roberts, Richard L; Sims, Harold; McLaughlin, Jacquelin E; Malkin, Robert A; Gardner, Carla D; Ni, Gemin; Rottman, Jeffrey N; Strauss, Arnold W (2003. ) Very-long-chain acyl-coenzyme a dehydrogenase deficiency in mice.Circulation research, , 93 (5 ) ,448-55 More Information

Spiekerkoetter, Ute; Sun, Bin; Zytkovicz, Thomas; Wanders, Ronald; Strauss, Arnold W; Wendel, Udo (2003. ) MS/MS-based newborn and family screening detects asymptomatic patients with very-long-chain acyl-CoA dehydrogenase deficiency.The Journal of pediatrics, , 143 (3 ) ,335-42 More Information

Shekhawat, Prem; Bennett, Michael J; Sadovsky, Yoel; Nelson, D Michael; Rakheja, Dinesh; Strauss, Arnold W (2003. ) Human placenta metabolizes fatty acids: implications for fetal fatty acid oxidation disorders and maternal liver diseases.American journal of physiology. Endocrinology and metabolism, , 284 (6 ) ,E1098-105 More Information

Spiekerkoetter, Ute; Sun, Bin; Khuchua, Zaza; Bennett, Michael J; Strauss, Arnold W (2003. ) Molecular and phenotypic heterogeneity in mitochondrial trifunctional protein deficiency due to beta-subunit mutations.Human mutation, , 21 (6 ) ,598-607 More Information

Strauss, Arnold; Lock, James E (2003. ) Pediatric cardiomyopathy--a long way to go.The New England journal of medicine, , 348 (17 ) ,1703-5 More Information

Spiekerkoetter, Ute; Eeds, Angela; Yue, Zou; Haines, Jonathan; Strauss, Arnold W; Summar, Marshall (2002. ) Uniparental disomy of chromosome 2 resulting in lethal trifunctional protein deficiency due to homozygous alpha-subunit mutations.Human mutation, , 20 (6 ) ,447-51 More Information

Yang, Zi; Yamada, Jennifer; Zhao, Yiwen; Strauss, Arnold W; Ibdah, Jamal A (2002. ) Prospective screening for pediatric mitochondrial trifunctional protein defects in pregnancies complicated by liver disease. JAMA : the journal of the American Medical Association, , 288 (17 ) ,2163-6

Yang, Zi; Zhao, Yiwen; Bennett, Michael J; Strauss, Arnold W; Ibdah, Jamal A (2002. ) Fetal genotypes and pregnancy outcomes in 35 families with mitochondrial trifunctional protein mutations. American journal of obstetrics and gynecology, , 187 (3 ) ,715-20

Straussberg, Rachel; Strauss, Arnold W (2002. ) A novel mutation of late-onset very-long-chain acyl-CoA dehydrogenase deficiency. Pediatric neurology, , 27 (2 ) ,136-7

Hintz, Susan R; Matern, Dietrich; Strauss, Arnold; Bennett, Michael J; Hoyme, H Eugene; Schelley, Susan; Kobori, Joyce; Colby, Christopher; Lehman, Norman L; Enns, Gregory M (2002. ) Early neonatal diagnosis of long-chain 3-hydroxyacyl coenzyme a dehydrogenase and mitochondrial trifunctional protein deficiencies.Molecular genetics and metabolism, , 75 (2 ) ,120-7 More Information

Strauss, Arnold W. (1998. ) The molecular basis of congenital cardiac disease. Seminars in thoracic and cardiovascular surgery. Pediatric cardiac surgery annual, , 1 ,179-188

Academic - Cincinnati Children's Hospital Medical Center
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Cincinnati  Ohio, 45229
Phone: 513-636-2942
arnold.strauss@cchmc.org